Common Cardiac Conditions
- ASD Surgery in Delhi
- VSD Surgery in Children in Delhi
- Best PDA Surgery in Delhi
- Coarctation of Aorta Treatment in Delhi
- Aortic Stenosis Treatment in Delhi
- Pulmonary Stenosis
- Atrio-Ventricular Septal Defect (AVSD/AVCD)
- RSOV Treatment in Delhi
- Eisenmenger Syndrome/ Complex
- Tetralogy of Fallot Treatment
- Transposition of Great Arteries (d-TGA)
- Total anomalous pulmonary venous connection treatment in Delhi
- Truncus Arteriosus
- Tricuspid Atresia
- Double Outlet Ventricle
- Congenitally Corrected Transposition of great vessels in Delhi
- Ebstein’s Anomaly
- Pulmonart Atresia (PA) Without VSD/Intact Septum
- Pulmonart Atresia (PA) with VSD
- Hypoplastic Left Heart Syndrome
- Stenosis of Pulmonary Artery Branches
- Patent Foramen Ovale (PFO)
- AP Window Device Closure
- Vascular Rings
- Interrupted Aortic Arch (IAA)
- Bicuspid Aortic Valve Treatment
- SVT treatment in children
Difference from PA with VSD?
In this condition, there is no connection between RV and LV as ventricular septum is intact. Most of the times, tricuspid valve (TV) is abnormal in this condition.
Treatment options in this condition?
Treatment is decided on the basis of size of TV. If TV size is small then RV will be very small and if it is adequate in size then RV will be of adequate in size. If size of RV is adequate then we may palliate the child by perforating the pulmonary valve by intervention (without surgery). If size of RV is small, then blood supply to the lungs will depend on PDA and by doing this if RV can grow in few days to weeks, then two ventricle repairs can be planned. PDA can be opened either by PGE1 (prostaglandin) infusion or by putting a stent into it.
How the child does presents clinically?
If size of RV is small then there will be tricuspid valve regurgitation and there will be reverse shunting across PFO and child will be blue from early period of life. If size of RV is very very small then RV pressure will be very high and there will be formation of coronary sinusoids in RV. In this condition, coronary circulation will depends on RV and we cannot open pulmonary valve in this situation.
What are other treatment options that we can do in this case?
Only superior vena cava (draining impure blood from upper part of body) can be connected to pulmonary artery leaving IVC (draining impure blood from lower part of body) drainage into RA (known as one and half ventricle repair). If RV size is also not able to tolerate this then only aspect is to do univentricular pathway treatment (Fontan operation).